IgG4 Inflammatory Pseudotumor of the Kidney

IgG4-related inflammatory pseudotumor of the renal pelvis involving renal parenchyma, mimicking malignancy

BACKGROUND IgG4-related disease is a recently recognized systemic disease characterized by storiform fibrosis with infiltration of IgG4-positive plasma cells. In rare incidences, IgG4-related renal disease can present as a solitary mass lesion at renal pelvis and can pose a diagnostic challenge since these lesions mimic malignancy. Herein, we present a rare case of IgG4-related disease presenti...

Erratum to “IgG4 Inflammatory Pseudotumor of the Kidney”

IgG4 related disease in pancreas, bile duct and liver

IgG4-related disease is a unique systemic inflammatory condition characterized by pseudotumorous formation or swelling of affected organs and high-serum IgG4 concentrations. Further studies have demonstrated that IgG4-related disease can involve a variety of organs including the pancreas ( type 1 autoimmune pancreatitis) , bile duct ( IgG4-related sclerosing cholangitis), liver (IgG4-related he...

IgG4-related tubulointerstitial nephritis and hepatic inflammatory pseudotumor without hypocomplementemia.

Immunoglobulin G4 (IgG4)-related tubulointerstitial nephritis (TIN) is often accompanied by autoimmune pancreatitis (AIP) or chronic sclerosing dacryoadenitis and sialoadenitis. However, IgG4-related TIN without AIP or lacrimal and/or salivary gland lesions has not been well recognized. Here, we report a case of IgG4-related TIN associated with hepatic inflammatory pseudotumor without AIP or la...

IgG4-related hepatic inflammatory pseudotumor with sclerosing cholangitis: a case report and review of the literature

INTRODUCTION Inflammatory pseudotumor is rare benign mass composed of chronic inflammatory cell infiltration and proliferating fibrous tissue. Some cases of inflammatory pseudotumor show abundant infiltrating IgG4-positive plasma cells and obliterative phlebitis, which are the pathologic hallmarks of autoimmune pancreatitis. CASE PRESENTATION A 77-year-old Japanese man was admitted to our hos...